U.S. flag

An official website of the United States government

Format

Send to:

Choose Destination

Primary Pigmented Nodular Adrenal Dysplasia

MedGen UID:
1382077
•Concept ID:
C4331029
•
Congenital Abnormality

Definition

A subtype of micronodular adrenal hyperplasia, characterized by multiple pigmented nodules, which may occur in isolation or as part of the Carney complex. [from NCI]

Term Hierarchy

CClinical test,  RResearch test,  OOMIM,  GGeneReviews,  VClinVar  
  • CROGVPrimary Pigmented Nodular Adrenal Dysplasia

Recent clinical studies

Etiology

CT and MR imaging of the adrenal glands in ACTH-independent cushing syndrome.
Rockall AG, Babar SA, Sohaib SA, Isidori AM, Diaz-Cano S, Monson JP, Grossman AB, Reznek RH
Radiographics 2004 Mar-Apr;24(2):435-52. doi: 10.1148/rg.242035092. PMID: 15026592

Diagnosis

Cushing's disease.
Bertagna X, Guignat L, Groussin L, Bertherat J
Best Pract Res Clin Endocrinol Metab 2009 Oct;23(5):607-23. doi: 10.1016/j.beem.2009.06.001. PMID: 19945026
ACTH-independent macronodular adrenal hyperplasia: imaging findings of a rare condition : A case report.
Verma A, Mohan S, Gupta A
Abdom Imaging 2008 Mar-Apr;33(2):225-9. doi: 10.1007/s00261-007-9236-y. PMID: 17502981
CT and MR imaging of the adrenal glands in ACTH-independent cushing syndrome.
Rockall AG, Babar SA, Sohaib SA, Isidori AM, Diaz-Cano S, Monson JP, Grossman AB, Reznek RH
Radiographics 2004 Mar-Apr;24(2):435-52. doi: 10.1148/rg.242035092. PMID: 15026592
An unusual cause of Cushing's syndrome: primary pigmented nodular adrenal dysplasia.
Sofat N, Turner J, Khoo B, Sohail M, Krausz T, Evans P, Meeran K
Int J Clin Pract 2000 May;54(4):269-71. PMID: 10912321

Therapy

ACTH-independent macronodular adrenal hyperplasia: imaging findings of a rare condition : A case report.
Verma A, Mohan S, Gupta A
Abdom Imaging 2008 Mar-Apr;33(2):225-9. doi: 10.1007/s00261-007-9236-y. PMID: 17502981

Prognosis

Cushing's disease.
Bertagna X, Guignat L, Groussin L, Bertherat J
Best Pract Res Clin Endocrinol Metab 2009 Oct;23(5):607-23. doi: 10.1016/j.beem.2009.06.001. PMID: 19945026

Supplemental Content

Table of contents

    Related information

    • PMC Articles
      Related information in PubMed Central Links
    • PubMed
      Related literature resources in PubMed

    Recent activity

    Clear Turn Off Turn On

    Your browsing activity is empty.

    Activity recording is turned off.

    Turn recording back on

    See more...